Right Aortic Arch

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Guy Sovak
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Right Aortic Arch

Dose any one know what is the prevalance of a Righ Aortic Arch in the population?

montgomj
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Pediatr Surg Int. 1999;15(1)

Pediatr Surg Int. 1999;15(1):28-31.

The frequency, significance, and management of a right aortic arch in association with esophageal atresia.

* Bowkett B,
* Beasley SW,
* Myers NA.

Department of Surgery, Wellington Hospital, P.O. Box 7902, Wellington, New Zealand.

An unrecognised right aortic arch (RAA) found at thoracotomy may complicate the repair of oesophageal atresia (OA) and tracheo-oesophageal fistula (TOF). This paper analyses the patient characteristics, peri-operative management, and outcome of 16 infants with a RAA, and proposes management guidelines. Between 1948 and 1996, 709 patients with OA/TOF were admitted to the Royal Children's Hospital, of whom 13 had a RAA. Three additional cases from two other paediatric surgical units were included. All 16 case records were reviewed retrospectively. The overall incidence of RAA in OA was 1.8%. Neither a chest radiograph in 16, nor antenatal ultrasonography in 7 detected a RAA. Post-natal echocardiography (ECHG) detected a RAA in only 1 of 7 infants examined; that patient underwent repair of the OA through a left (L) thoracotomy. The other 15 infants underwent initial right (R) thoracotomy. Six of these had a complete repair from the R side and 5 had division of the fistula only; 2 of these 5 had initial division of the fistula, and the OA was repaired through a repeat R thoracotomy 4 and 7 weeks later. In the remaining 4 infants where the fistula could not be located at the initial R thoracotomy, complete repair proved possible through the L chest. Three of these infants underwent an immediate L thoracotomy; the 4th had a delayed L thoracotomy 1 week later. There were 6 deaths: these occurred early in the study and were related to severe prematurity, congenital heart disease (CHD), and post-operative respiratory complications. CHD was identified in 11 of 16 infants (71%). Routine pre-operative ECHG is unreliable in determining the laterality of the aortic arch. Should a RAA be encountered during a R thoracotomy for OA, it is often possible to divide the fistula and repair the OA from that side, but where repair looks potentially difficult it is wise to proceed to an immediate L thoracotomy.

montgomj
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This is a quote directly from

This is a quote directly from "Abnormalities of the Human Heart"

http://www.orpha.net/data/patho/GB/uk-aortic-arch.pdf

"Vascular rings ar uncommon anomalies and make up less than 1% of congenital cardiac defects. They occur with about equal frequency in both sexes. No geographical or racial predominance exists. The 2 most common types of complete vascular rings are double aortic arch and right aortic arch with left ligamentum arteriosum. These make up 85-95% of the cases."

Guy Sovak
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Thank you for the information

Thank you for the information,
1% out of the population for all Aortic Arch abnormalities.
Once again thank you .
Guy